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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
AUTOPHAGY
Atrophy
Effector T cells
Annexin A2
Dystrophin
Myopathies
Myoblast
Thérapie génique
Regulatory T cells
DMD
2-D PAGE
BINDING SPECIFICITY
Neuromuscular disease
Antiserum
Dysferlin
Lamins
Neuromuscular junction NMJ
Oculopharyngeal muscular dystrophy
Sarcopenia
MUTATIONS
Amyotrophic Lateral Sclerosis
ARN
Biomarker
AAV vectors
Dystrophie musculaire oculopharyngée
DUX4
Andermann syndrome
Akt
Omics
Myopathy
Ageing
Regenerative medicine
Actin
Myositis
Myotube
Bile salt hydrolases
Satellite cell
Fibrosis
Metabolism
Anti-acetylcholine receptor antibodies
Duchenne muscular dystrophy
Satellite cells
GENE
RNA
Dysferlinopathy
Autologous
Arbovirus
Cross-bridge kinetics
Intercellular communication
Differentiation
AChR antibodies
Adipose tissue
Alphavirus
Functional genomics
Regeneration
Exon-skipping
Geriatric assessment
Calcium
OPMD
PABPN1 agregates
Skeletal muscle
Agrégats de PABPN1
APOPTOSIS
Inflammation
Aged
Myosin
Human
FSHD
Pax7
Anti-fibrotic pharmacotherapies
Aav-U7
Muscular dystrophy
AAV
Muscle stem cells
Xenograft
Myogenesis
Haploinsufficiency
Cell therapy
ALS
Muscle dystrophy
FAPs
Muscle
Alzheimer's disease
Transcriptomics
Pharyngeal muscle
Antisens oligonucleotides
Accelerometry
Nuclear envelope
Triplet expansion disease
Gene therapy
Aggregate
Muscle fibrosis
Epigenetics
Autoimmune diseases
DNA methylation
Myoblasts
Mass spectrometry
Muscle strength
Gene replacement
PABPN1